{"id":3107,"date":"2022-10-15T15:28:29","date_gmt":"2022-10-15T15:28:29","guid":{"rendered":"https:\/\/neuropediatoolbox.org\/?p=3107"},"modified":"2026-06-22T16:28:05","modified_gmt":"2026-06-22T16:28:05","slug":"sindrome-de-dyke-davidoff-masson","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/de\/sindrome-de-dyke-davidoff-masson\/","title":{"rendered":"Dyke-Davidoff-Masson-Syndrom."},"content":{"rendered":"<p class=\"wp-block-paragraph\">Er <a href=\"https:\/\/radiopaedia.org\/articles\/dyke-davidoff-masson-syndrome\">Dyke-Davidoff-Masson-Syndrom<\/a> Es handelt sich um ein spezifisch p\u00e4diatrisches Syndrom, das durch eine hemizebrale Atrophie oder Hypoplasie als Folge einer Hirnsch\u00e4digung gekennzeichnet ist, meist in der fetalen Periode oder in der fr\u00fchen Kindheit, weshalb es von einer damit verbundenen Sch\u00e4delwachstumsst\u00f6rung begleitet wird, die durch eine kompensatorische ipsilaterale Knochenhypertrophie und Hyperpneumatisierung der Nasen- und Stirnh\u00f6hlen sowie die neurologischen Folgen der Sch\u00e4digung in Form einer kontralateralen Hemiparese und\/oder epileptischen Anf\u00e4llen gekennzeichnet ist. <\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Dies erh\u00f6ht die Differenzialdiagnose zu anderen Ursachen einer Hemisph\u00e4rischen Asymmetrie, wie Rasmussen-Enzephalitis oder Hemimegalenzephalie (es gibt keine kompensatorische ipsilaterale Knochenhypertrophie).<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full is-resized\"><img fetchpriority=\"high\" decoding=\"async\" src=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40.png\" alt=\"\" class=\"wp-image-3190\" width=\"621\" height=\"580\" srcset=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40.png 803w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40-300x280.png 300w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40-768x717.png 768w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40-13x12.png 13w\" sizes=\"(max-width: 621px) 100vw, 621px\" \/><figcaption>Hemimegalenzephalie. <\/figcaption><\/figure>\n<\/div>\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full\"><img decoding=\"async\" width=\"630\" height=\"630\" src=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41.png\" alt=\"\" class=\"wp-image-3192\" srcset=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41.png 630w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41-150x150.png 150w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41-300x300.png 300w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41-12x12.png 12w\" sizes=\"(max-width: 630px) 100vw, 630px\" \/><figcaption>Rasmussen-Enzephalitis.<\/figcaption><\/figure>\n<\/div>\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full is-resized\"><img decoding=\"async\" src=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42.png\" alt=\"\" class=\"wp-image-3193\" width=\"628\" height=\"744\" srcset=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42.png 532w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42-253x300.png 253w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42-10x12.png 10w\" sizes=\"(max-width: 628px) 100vw, 628px\" \/><figcaption>Dyke-Davidoff-Masson-Syndrom. <\/figcaption><\/figure>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Das Dyke-Davidoff-Masson-Syndrom ist ein spezifisch p\u00e4diatrisches Syndrom, das durch eine hemizebrale Atrophie oder Hypoplasie als Folge einer Hirnsch\u00e4digung, meist in der fetalen Periode oder in der fr\u00fchen Kindheit, gekennzeichnet ist. Deshalb geht es mit einer damit verbundenen Sch\u00e4delwachstumsst\u00f6rung einher, die durch kompensatorische ipsilaterale Knochenhypertrophie und Hyperpneumatisierung der Nasennebenh\u00f6hlen gekennzeichnet ist. <\/p>\n<p class=\"link-more\"><a href=\"https:\/\/neuropediatoolkit.org\/de\/sindrome-de-dyke-davidoff-masson\/\" class=\"more-link\">Lesen Sie weiter<span class=\"screen-reader-text\"> \u201eDyke-Davidoff-Masson-Syndrom.\u201c<\/span><\/a><\/p>","protected":false},"author":1,"featured_media":3193,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[3,48],"tags":[],"class_list":["post-3107","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-enfermedades-neurologicas","category-especificamente-pediatricos","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts\/3107","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/comments?post=3107"}],"version-history":[{"count":1,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts\/3107\/revisions"}],"predecessor-version":[{"id":8200,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts\/3107\/revisions\/8200"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/media\/3193"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/media?parent=3107"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/categories?post=3107"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/tags?post=3107"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}