{"id":6313,"date":"2023-08-04T16:36:49","date_gmt":"2023-08-04T16:36:49","guid":{"rendered":"https:\/\/neuropediaclinic.com\/?p=6313"},"modified":"2023-08-04T16:39:25","modified_gmt":"2023-08-04T16:39:25","slug":"coenzima-q10-decorenone","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/de\/coenzima-q10-decorenone\/","title":{"rendered":"Coenzym Q10 (Decorenon)."},"content":{"rendered":"<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full\">https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10\">https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona\">https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Behandlungsindikationen in der p\u00e4diatrischen Neurologie: <\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Mitochondriale Erkrankungen: \n<ul class=\"wp-block-list\">\n<li>Angeborener (prim\u00e4rer) Coenzym-Q10-Mangel. Symptome in Form von zerebell\u00e4rer Ataxie, Enzephalomyopathie und isolierter Myopathie. <\/li>\n\n\n\n<li>Andere mitochondriale Erkrankungen (sekund\u00e4rer Mangel): \n<ul class=\"wp-block-list\">\n<li>Friedrich-Ataxie.<\/li>\n\n\n\n<li>CPEO (chronisch-progressive externe Ophthalmoplegie),<\/li>\n\n\n\n<li>Defekt des mitochondrialen Komplexes I. <\/li>\n\n\n\n<li>Mangel des Mitochondrienkomplexes II. <\/li>\n\n\n\n<li>Defekt des Mitochondrienkomplexes II\/IV. <\/li>\n\n\n\n<li>Kearns-Sayre-Syndrom. <\/li>\n\n\n\n<li>LHON (Leber\u2019sche heredit\u00e4re Optikusneuropathie).<\/li>\n\n\n\n<li>MELAS (Mitochondriale Myopathie, Enzephalopathie, Laktatazidose und schlaganfall\u00e4hnliche Symptome).<\/li>\n\n\n\n<li>NARP (neurogene Muskelschw\u00e4che, Ataxie und Retinitis pigmentosa).<\/li>\n\n\n\n<li>Ver\u00e4nderungen bei Twinkle (C10orf2)<\/li>\n\n\n\n<li>Okulomotorische Apraxie. <\/li>\n\n\n\n<li>Mitochondriale Kardiomyopathie. <\/li>\n\n\n\n<li>Alpers-Syndrom. <\/li>\n\n\n\n<li>MERRF (Myoklonische Epilepsie in Verbindung mit zerkl\u00fcfteten roten Fasern).<\/li>\n\n\n\n<li>SANDO (Sensorische Ataxie mit Neuropathie, Dysarthrie und Ophthalmoparese)<\/li>\n\n\n\n<li>Mitochondriales DNA-Depletionssyndrom. <\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<\/li>\n\n\n\n<li>Sonstige Erkrankungen (sekund\u00e4rer Mangel): \n<ul class=\"wp-block-list\">\n<li>Propionazid\u00e4mie. <\/li>\n\n\n\n<li>Multisystemische Atrophie. <\/li>\n\n\n\n<li>Kortikobasale Degeneration. <\/li>\n\n\n\n<li>Muskeldystrophie. <\/li>\n\n\n\n<li>Amyotrophe Lateralsklerose. <\/li>\n\n\n\n<li>Multiple Sklerose. <\/li>\n\n\n\n<li>Charcot-Marie-Tooth-Krankheit.<\/li>\n\n\n\n<li>McArdle-Syndrom. <\/li>\n\n\n\n<li>Leukodystrophie. <\/li>\n\n\n\n<li>Migr\u00e4ne. <\/li>\n\n\n\n<li>Myopathie aufgrund eines Mangels an Mioadenilat-Desaminase (MADA). <\/li>\n\n\n\n<li>Progressive supranukle\u00e4re L\u00e4hmung. <\/li>\n\n\n\n<li>Syndrom des zyklischen Erbrechens. <\/li>\n\n\n\n<li>Sanfilippo-Syndrom. <\/li>\n\n\n\n<li>Wolf-Hirschhorn-Syndrom. <\/li>\n\n\n\n<li>Bardet-Biedl-Syndrom. <\/li>\n\n\n\n<li>Chronisches Ersch\u00f6pfungssyndrom. <\/li>\n\n\n\n<li>Schlaganfall. <\/li>\n\n\n\n<li>Adrenoleukodystrophie. <\/li>\n\n\n\n<li>Spinozerebell\u00e4re Ataxie. <\/li>\n\n\n\n<li>Fols\u00e4uremangel.<\/li>\n\n\n\n<li>Okulopharyngeale Dystrophie. <\/li>\n\n\n\n<li>Myotonische Dystrophie nach Steinert. <\/li>\n\n\n\n<li>Huntington-Krankheit. <\/li>\n\n\n\n<li>Niemann-Pick-Krankheit.<\/li>\n\n\n\n<li>Pompe-Krankheit. <\/li>\n\n\n\n<li>Spastik. <\/li>\n\n\n\n<li>Spastische Paraparese. <\/li>\n\n\n\n<li>Prader-Willi-Syndrom. <\/li>\n\n\n\n<li>Wolfram-Syndrom. <\/li>\n<\/ul>\n<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10 https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona Indicaciones de tratamiento en neurolog\u00eda pedi\u00e1trica:<\/p>","protected":false},"author":1,"featured_media":6314,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[24,7,17],"tags":[],"class_list":["post-6313","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-farmacos","category-metabolismo","category-tratamiento","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts\/6313","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/comments?post=6313"}],"version-history":[{"count":2,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts\/6313\/revisions"}],"predecessor-version":[{"id":6316,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/posts\/6313\/revisions\/6316"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/media\/6314"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/media?parent=6313"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/categories?post=6313"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/de\/wp-json\/wp\/v2\/tags?post=6313"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}