{"id":6313,"date":"2023-08-04T16:36:49","date_gmt":"2023-08-04T16:36:49","guid":{"rendered":"https:\/\/neuropediaclinic.com\/?p=6313"},"modified":"2023-08-04T16:39:25","modified_gmt":"2023-08-04T16:39:25","slug":"coenzima-q10-decorenone","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/en\/coenzima-q10-decorenone\/","title":{"rendered":"Coenzyme Q10 (Decorenone)."},"content":{"rendered":"<p><a href=\"https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full\">https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full<\/a><\/p>\n\n\n\n<p><a href=\"https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10\">https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10<\/a><\/p>\n\n\n\n<p><a href=\"https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona\">https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona<\/a><\/p>\n\n\n\n<p>Indicaciones de tratamiento en neurolog\u00eda pedi\u00e1trica: <\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Enfermedades mitocondriales: \n<ul class=\"wp-block-list\">\n<li>Deficiencia cong\u00e9nita de coenzima Q10 (primaria). S\u00edntomas en forma de ataxia cerebelosa, encefalomiopat\u00eda, miopat\u00eda aislada. <\/li>\n\n\n\n<li>Otras enfermedades mitocondriales (d\u00e9ficit secundario): \n<ul class=\"wp-block-list\">\n<li>Ataxia de Friedrich.<\/li>\n\n\n\n<li>CPEO (Chronic Progressive External Ophthalmoplegia),<\/li>\n\n\n\n<li>Deficiencia del complejo mitocondrial I. <\/li>\n\n\n\n<li>Deficiencia del complejo mitocondrial II. <\/li>\n\n\n\n<li>Deficiencia del complejo mitocondrial II\/IV. <\/li>\n\n\n\n<li>S\u00edndrome de Kearns-Sayre. <\/li>\n\n\n\n<li>LHON (Leber \u0301s Hereditary Optic Neuropathy).<\/li>\n\n\n\n<li>MELAS (Mitochondrial myopathy, Encephalopathy, Lactic Acidosis and Stroke-like).<\/li>\n\n\n\n<li>NARP (Neurogenic muscle weakness, Ataxia, and Retinitis Pigmentosa).<\/li>\n\n\n\n<li>Alteraciones de Twinkle (C10orf2)<\/li>\n\n\n\n<li>Apraxia oculomotora. <\/li>\n\n\n\n<li>Cardiomiopat\u00eda mitocondrial. <\/li>\n\n\n\n<li>Enfermedad de Alpers. <\/li>\n\n\n\n<li>MERRF (Myoclonic Epilepsyassociated with Ragged Red Fibers).<\/li>\n\n\n\n<li>SANDO (Sensory Ataxia with Neuropathy, Dysarthria and Ophthalmoparesis)<\/li>\n\n\n\n<li>S\u00edndrome de depleci\u00f3n del ADN mitocondrial. <\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<\/li>\n\n\n\n<li>Otras enfermedades (d\u00e9ficit secundario): \n<ul class=\"wp-block-list\">\n<li>Acidemia propi\u00f3nica. <\/li>\n\n\n\n<li>Atrofia multisist\u00e9mica. <\/li>\n\n\n\n<li>Degeneraci\u00f3n corticobasal. <\/li>\n\n\n\n<li>Distrofia muscular. <\/li>\n\n\n\n<li>Esclerosis lateral amiotr\u00f3fica. <\/li>\n\n\n\n<li>Esclerosis m\u00faltiple. <\/li>\n\n\n\n<li>Enfermedad de Charcot-Marie-Tooth.<\/li>\n\n\n\n<li>Enfermedad de McArdle. <\/li>\n\n\n\n<li>Leucodistrofia. <\/li>\n\n\n\n<li>Migra\u00f1a. <\/li>\n\n\n\n<li>Miopat\u00eda por d\u00e9ficit de mioadenilato desaminasa (MADA). <\/li>\n\n\n\n<li>Par\u00e1lisis supranuclear progresiva. <\/li>\n\n\n\n<li>S\u00edndrome de v\u00f3mitos c\u00edclicos. <\/li>\n\n\n\n<li>S\u00edndrome de Sanfilippo. <\/li>\n\n\n\n<li>S\u00edndrome de Wolf-Hirschhorn. <\/li>\n\n\n\n<li>S\u00edndrome de Bardet-Biedl. <\/li>\n\n\n\n<li>S\u00edndrome de fatiga cr\u00f3nica. <\/li>\n\n\n\n<li>Accidente cerebrovascular. <\/li>\n\n\n\n<li>Adrenoleucodistrofia. <\/li>\n\n\n\n<li>Ataxia espinocerebelosa. <\/li>\n\n\n\n<li>Deficiencia de \u00e1cido f\u00f3lico.<\/li>\n\n\n\n<li>Distrofia oculofar\u00edngea. <\/li>\n\n\n\n<li>Distrofia miot\u00f3nica de Steinert. <\/li>\n\n\n\n<li>Enfermedad de Huntington. <\/li>\n\n\n\n<li>Enfermedad de Niemann-Pick.<\/li>\n\n\n\n<li>Enfermedad de Pompe. <\/li>\n\n\n\n<li>Espasticidad. <\/li>\n\n\n\n<li>Paraparesia esp\u00e1stica. <\/li>\n\n\n\n<li>S\u00edndrome de Prader-Willi. <\/li>\n\n\n\n<li>S\u00edndrome de Wolfram. <\/li>\n<\/ul>\n<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10 https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona Indicaciones de tratamiento en neurolog\u00eda pedi\u00e1trica:<\/p>","protected":false},"author":1,"featured_media":6314,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[24,7,17],"tags":[],"class_list":["post-6313","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-farmacos","category-metabolismo","category-tratamiento","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts\/6313","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/comments?post=6313"}],"version-history":[{"count":2,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts\/6313\/revisions"}],"predecessor-version":[{"id":6316,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts\/6313\/revisions\/6316"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/media\/6314"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/media?parent=6313"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/categories?post=6313"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/tags?post=6313"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}