{"id":6313,"date":"2023-08-04T16:36:49","date_gmt":"2023-08-04T16:36:49","guid":{"rendered":"https:\/\/neuropediaclinic.com\/?p=6313"},"modified":"2023-08-04T16:39:25","modified_gmt":"2023-08-04T16:39:25","slug":"coenzima-q10-decorenone","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/en\/coenzima-q10-decorenone\/","title":{"rendered":"Coenzyme Q10 (Decorenone)."},"content":{"rendered":"<p><a href=\"https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full\">https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full<\/a><\/p>\n\n\n\n<p><a href=\"https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10\">https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10<\/a><\/p>\n\n\n\n<p><a href=\"https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona\">https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona<\/a><\/p>\n\n\n\n<p>Indications for treatment in pediatric neurology: <\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Mitochondrial diseases: \n<ul class=\"wp-block-list\">\n<li>Congenital coenzyme Q10 deficiency (primary). Symptoms in the form of cerebellar ataxia, encephalomyopathy, isolated myopathy. <\/li>\n\n\n\n<li>Other mitochondrial diseases (secondary deficiency): \n<ul class=\"wp-block-list\">\n<li>Friedrich's ataxia.<\/li>\n\n\n\n<li>CPEO (Chronic Progressive External Ophthalmoplegia),<\/li>\n\n\n\n<li>Mitochondrial complex I deficiency. <\/li>\n\n\n\n<li>Mitochondrial complex II deficiency. <\/li>\n\n\n\n<li>Mitochondrial complex II\/IV deficiency. <\/li>\n\n\n\n<li>Kearns-Sayre syndrome. <\/li>\n\n\n\n<li>LHON (Leber's Hereditary Optic Neuropathy).<\/li>\n\n\n\n<li>MELAS (Mitochondrial myopathy, Encephalopathy, Lactic Acidosis and Stroke-like).<\/li>\n\n\n\n<li>NARP (Neurogenic muscle weakness, Ataxia, and Retinitis Pigmentosa).<\/li>\n\n\n\n<li>Twinkle disorders (C10orf2)<\/li>\n\n\n\n<li>Oculomotor apraxia. <\/li>\n\n\n\n<li>Mitochondrial cardiomyopathy. <\/li>\n\n\n\n<li>Alpers disease. <\/li>\n\n\n\n<li>MERRF (Myoclonic Epilepsy associated with Ragged Red Fibers).<\/li>\n\n\n\n<li>SANDO (Sensory Ataxia with Neuropathy, Dysarthria and Ophthalmoparesis)<\/li>\n\n\n\n<li>Mitochondrial DNA depletion syndrome. <\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<\/li>\n\n\n\n<li>Other diseases (secondary deficiency): \n<ul class=\"wp-block-list\">\n<li>Propionic acidemia. <\/li>\n\n\n\n<li>Multiple system atrophy. <\/li>\n\n\n\n<li>Corticobasal degeneration. <\/li>\n\n\n\n<li>Muscular dystrophy. <\/li>\n\n\n\n<li>Amyotrophic lateral sclerosis. <\/li>\n\n\n\n<li>Multiple sclerosis. <\/li>\n\n\n\n<li>Charcot-Marie-Tooth disease.<\/li>\n\n\n\n<li>McArdle disease. <\/li>\n\n\n\n<li>Leukodystrophy. <\/li>\n\n\n\n<li>Migraine. <\/li>\n\n\n\n<li>Myopathy due to myoadenylate deaminase (MADA) deficiency. <\/li>\n\n\n\n<li>Progressive supranuclear palsy. <\/li>\n\n\n\n<li>Cyclic vomiting syndrome. <\/li>\n\n\n\n<li>Sanfilippo syndrome. <\/li>\n\n\n\n<li>Wolf-Hirschhorn syndrome. <\/li>\n\n\n\n<li>Bardet-Biedl syndrome. <\/li>\n\n\n\n<li>Chronic fatigue syndrome. <\/li>\n\n\n\n<li>Stroke. <\/li>\n\n\n\n<li>Adrenoleukodystrophy. <\/li>\n\n\n\n<li>Spinocerebellar ataxia. <\/li>\n\n\n\n<li>Folic acid deficiency.<\/li>\n\n\n\n<li>Oculopharyngeal dystrophy. <\/li>\n\n\n\n<li>Steinert myotonic dystrophy. <\/li>\n\n\n\n<li>Huntington's disease. <\/li>\n\n\n\n<li>Niemann-Pick disease.<\/li>\n\n\n\n<li>Pompe disease. <\/li>\n\n\n\n<li>Spasticity. <\/li>\n\n\n\n<li>Spastic paraparesis. <\/li>\n\n\n\n<li>Prader-Willi syndrome. <\/li>\n\n\n\n<li>Wolfram syndrome. <\/li>\n<\/ul>\n<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10 https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona Indicaciones de tratamiento en neurolog\u00eda pedi\u00e1trica:<\/p>","protected":false},"author":1,"featured_media":6314,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[24,7,17],"tags":[],"class_list":["post-6313","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-farmacos","category-metabolismo","category-tratamiento","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts\/6313","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/comments?post=6313"}],"version-history":[{"count":2,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts\/6313\/revisions"}],"predecessor-version":[{"id":6316,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/posts\/6313\/revisions\/6316"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/media\/6314"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/media?parent=6313"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/categories?post=6313"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/en\/wp-json\/wp\/v2\/tags?post=6313"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}