{"id":3107,"date":"2022-10-15T15:28:29","date_gmt":"2022-10-15T15:28:29","guid":{"rendered":"https:\/\/neuropediatoolbox.org\/?p=3107"},"modified":"2026-06-22T16:28:05","modified_gmt":"2026-06-22T16:28:05","slug":"sindrome-de-dyke-davidoff-masson","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/fr\/sindrome-de-dyke-davidoff-masson\/","title":{"rendered":"Syndrome de Dyke-Davidoff-Masson."},"content":{"rendered":"<p>Il <a href=\"https:\/\/radiopaedia.org\/articles\/dyke-davidoff-masson-syndrome\">Syndrome de Dyke-Davidoff-Masson<\/a> Il s'agit d'un syndrome sp\u00e9cifiquement p\u00e9diatrique caract\u00e9ris\u00e9 par une atrophie h\u00e9mic\u00e9r\u00e9brale ou une hypoplasie secondaire \u00e0 une agression c\u00e9r\u00e9brale, g\u00e9n\u00e9ralement pendant la p\u00e9riode f\u0153tale ou dans la petite enfance, c'est pourquoi il s'accompagne d'un trouble de la croissance cr\u00e2nienne associ\u00e9, caract\u00e9ris\u00e9 par une hypertrophie osseuse homolat\u00e9rale compensatoire et une hyperpneumatisation des sinus nasaux et frontaux, et des cons\u00e9quences neurologiques de l'agression, sous forme d'h\u00e9mipar\u00e9sie controlat\u00e9rale et\/ou de crises d'\u00e9pilepsie. <\/p>\n\n\n\n<p>Il pose le diagnostic diff\u00e9rentiel avec d'autres causes d'asym\u00e9trie h\u00e9misph\u00e9rique, comme l'enc\u00e9phalite de Rasmussen ou l'h\u00e9mim\u00e9galenc\u00e9phalie (il n'y a pas d'hypertrophie osseuse homolat\u00e9rale compensatoire).<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full is-resized\"><img fetchpriority=\"high\" decoding=\"async\" src=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40.png\" alt=\"\" class=\"wp-image-3190\" width=\"621\" height=\"580\" srcset=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40.png 803w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40-300x280.png 300w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40-768x717.png 768w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-40-13x12.png 13w\" sizes=\"(max-width: 621px) 100vw, 621px\" \/><figcaption>H\u00e9mim\u00e9galenc\u00e9phalie. <\/figcaption><\/figure>\n<\/div>\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full\"><img decoding=\"async\" width=\"630\" height=\"630\" src=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41.png\" alt=\"\" class=\"wp-image-3192\" srcset=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41.png 630w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41-150x150.png 150w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41-300x300.png 300w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-41-12x12.png 12w\" sizes=\"(max-width: 630px) 100vw, 630px\" \/><figcaption>Enc\u00e9phalite de Rasmussen.<\/figcaption><\/figure>\n<\/div>\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full is-resized\"><img decoding=\"async\" src=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42.png\" alt=\"\" class=\"wp-image-3193\" width=\"628\" height=\"744\" srcset=\"https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42.png 532w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42-253x300.png 253w, https:\/\/neuropediatoolkit.org\/wp-content\/uploads\/2022\/10\/image-42-10x12.png 10w\" sizes=\"(max-width: 628px) 100vw, 628px\" \/><figcaption>Syndrome de Dyke-Davidoff-Masson. <\/figcaption><\/figure>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>Le syndrome de Dyke-Davidoff-Masson est un syndrome sp\u00e9cifiquement p\u00e9diatrique caract\u00e9ris\u00e9 par une atrophie h\u00e9mic\u00e9r\u00e9brale ou une hypoplasie secondaire \u00e0 une atteinte c\u00e9r\u00e9brale g\u00e9n\u00e9ralement survenue pendant la p\u00e9riode f\u0153tale ou dans la petite enfance, c'est pourquoi il s'accompagne d'un trouble de la croissance cr\u00e2nienne associ\u00e9, caract\u00e9ris\u00e9 par une hypertrophie osseuse homolat\u00e9rale compensatoire et une hyperpneumatisation des sinus nasaux... <\/p>\n<p class=\"link-more\"><a href=\"https:\/\/neuropediatoolkit.org\/fr\/sindrome-de-dyke-davidoff-masson\/\" class=\"more-link\">Continue reading<span class=\"screen-reader-text\"> \u00abS\u00edndrome de Dyke-Davidoff-Masson.\u00bb<\/span><\/a><\/p>","protected":false},"author":1,"featured_media":3193,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[3,48],"tags":[],"class_list":["post-3107","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-enfermedades-neurologicas","category-especificamente-pediatricos","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/posts\/3107","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/comments?post=3107"}],"version-history":[{"count":1,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/posts\/3107\/revisions"}],"predecessor-version":[{"id":8200,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/posts\/3107\/revisions\/8200"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/media\/3193"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/media?parent=3107"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/categories?post=3107"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/fr\/wp-json\/wp\/v2\/tags?post=3107"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}