{"id":4523,"date":"2023-02-19T18:10:27","date_gmt":"2023-02-19T18:10:27","guid":{"rendered":"https:\/\/neuropediatoolbox.org\/?p=4523"},"modified":"2026-06-22T16:28:58","modified_gmt":"2026-06-22T16:28:58","slug":"trayectoria-de-desarrollo-de-la-mld-leucodistrofia-metacromatica","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/ja\/trayectoria-de-desarrollo-de-la-mld-leucodistrofia-metacromatica\/","title":{"rendered":"MLD\uff08\u7570\u67d3\u6027\u767d\u8cea\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc\uff09\u306e\u767a\u75c7\u306e\u8ecc\u8de1\u3002"},"content":{"rendered":"<h2 class=\"wp-block-heading\">\u7570\u67d3\u6027\u767d\u8cea\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc (MLD): \u767a\u9054\u306e\u8ecc\u8de1<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">\u7570\u67d3\u6027\u767d\u8cea\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc\u306f\u3001\u9175\u7d20\u30a2\u30ea\u30fc\u30eb\u30b9\u30eb\u30d5\u30a1\u30bf\u30fc\u30bc A (ARSA) \u306e\u6b20\u640d\u3092\u7279\u5fb4\u3068\u3059\u308b\u5e38\u67d3\u8272\u4f53\u52a3\u6027\u907a\u4f1d\u6027\u30ea\u30bd\u30bd\u30fc\u30e0\u84c4\u7a4d\u75c7\u3067\u3001\u30b9\u30eb\u30d5\u30a1\u30c1\u30c9\u306e\u84c4\u7a4d\u3068\u4e2d\u67a2\u795e\u7d4c\u7cfb\u304a\u3088\u3073\u672b\u68a2\u795e\u7d4c\u7cfb\u306e\u9032\u884c\u6027\u8131\u9ac4\u3092\u5f15\u304d\u8d77\u3053\u3057\u307e\u3059\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">\u81e8\u5e8a\u5f62\u614b\u3068\u7d4c\u904e<\/h3>\n\n\n\n<ul class=\"wp-block-list\">\n    <li><strong>\u5f8c\u671f\u4e73\u5150 (\u5178\u578b\u7684):<\/strong> \u751f\u5f8c1\u5e74\u76ee\u304b\u30892\u5e74\u76ee\u306b\u304b\u3051\u3066\u767a\u75c7\u3057\u307e\u3059\u3002\u4e73\u5150\u306f\u7372\u5f97\u3057\u305f\u6b69\u884c\u80fd\u529b\u3092\u5931\u3044\u3001\u91cd\u5ea6\u306e\u904b\u52d5\u9000\u884c\u3001\u9032\u884c\u6027\u306e\u75d9\u6027\u56db\u80a2\u4e0d\u5168\u9ebb\u75fa\u3001\u304a\u3088\u3073\u5931\u660e\u3092\u793a\u3057\u307e\u3059\u3002<\/li>\n    <li><strong>\u82e5\u8005\u3068\u5927\u4eba:<\/strong> \u9032\u884c\u306f\u9045\u304f\u3001\u6700\u521d\u306f\u5b66\u7fd2\u56f0\u96e3\u3001\u884c\u52d5\u969c\u5bb3\u3001\u904b\u52d5\u5931\u8abf\u3001\u305d\u306e\u5f8c\u306e\u5168\u4f53\u7684\u306a\u904b\u52d5\u969c\u5bb3\u3092\u7279\u5fb4\u3068\u3057\u307e\u3059\u3002<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>\u7570\u67d3\u6027\u767d\u8cea\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc (MLD): \u767a\u751f\u306e\u8ecc\u8de1 \u7570\u67d3\u6027\u767d\u8cea\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc\u306f\u3001\u9175\u7d20\u30a2\u30ea\u30fc\u30eb\u30b9\u30eb\u30d5\u30a1\u30bf\u30fc\u30bc A (ARSA) \u306e\u6b20\u640d\u3092\u7279\u5fb4\u3068\u3059\u308b\u5e38\u67d3\u8272\u4f53\u52a3\u6027\u907a\u4f1d\u306e\u30ea\u30bd\u30bd\u30fc\u30e0\u84c4\u7a4d\u75c7\u3067\u3001\u30b9\u30eb\u30d5\u30a1\u30c1\u30c9\u306e\u84c4\u7a4d\u3068\u4e2d\u67a2\u795e\u7d4c\u7cfb\u304a\u3088\u3073\u672b\u68a2\u795e\u7d4c\u7cfb\u306e\u9032\u884c\u6027\u8131\u9ac4\u3092\u5f15\u304d\u8d77\u3053\u3057\u307e\u3059\u3002\u81e8\u5e8a\u5f62\u614b\u3068\u5c0f\u5150\u671f\u5f8c\u671f\u306e\u8ecc\u8de1\uff08\u5178\u578b\u7684\uff09\uff1a\u305d\u308c\u306f\u3001\u6700\u521d\u306e\u2026 <\/p>\n<p class=\"link-more\"><a href=\"https:\/\/neuropediatoolkit.org\/ja\/trayectoria-de-desarrollo-de-la-mld-leucodistrofia-metacromatica\/\" class=\"more-link\">\u7d9a\u304d\u3092\u8aad\u3080<span class=\"screen-reader-text\"> \u300cMLD\uff08\u7570\u67d3\u6027\u767d\u8cea\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc\uff09\u306e\u767a\u75c7\u306e\u8ecc\u8de1\u300d\u3002<\/span><\/a><\/p>","protected":false},"author":1,"featured_media":4525,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[49],"tags":[],"class_list":["post-4523","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-neurodegenerativas","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/posts\/4523","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/comments?post=4523"}],"version-history":[{"count":2,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/posts\/4523\/revisions"}],"predecessor-version":[{"id":8292,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/posts\/4523\/revisions\/8292"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/media\/4525"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/media?parent=4523"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/categories?post=4523"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ja\/wp-json\/wp\/v2\/tags?post=4523"}],"curies":[{"name":"\u3046\u30fc\u3093","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}