{"id":6313,"date":"2023-08-04T16:36:49","date_gmt":"2023-08-04T16:36:49","guid":{"rendered":"https:\/\/neuropediaclinic.com\/?p=6313"},"modified":"2023-08-04T16:39:25","modified_gmt":"2023-08-04T16:39:25","slug":"coenzima-q10-decorenone","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/ru\/coenzima-q10-decorenone\/","title":{"rendered":"\u041a\u043e\u044d\u043d\u0437\u0438\u043c Q10 (\u0414\u0435\u043a\u043e\u0440\u0435\u043d\u043e\u043d)."},"content":{"rendered":"<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full\">https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10\">https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\"><a href=\"https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona\">https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona<\/a><\/p>\n\n\n\n<p class=\"wp-block-paragraph\">\u041f\u043e\u043a\u0430\u0437\u0430\u043d\u0438\u044f \u043a \u043b\u0435\u0447\u0435\u043d\u0438\u044e \u0432 \u0434\u0435\u0442\u0441\u043a\u043e\u0439 \u043d\u0435\u0432\u0440\u043e\u043b\u043e\u0433\u0438\u0438: <\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>\u041c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u044b\u0435 \u0437\u0430\u0431\u043e\u043b\u0435\u0432\u0430\u043d\u0438\u044f: \n<ul class=\"wp-block-list\">\n<li>\u0412\u0440\u043e\u0436\u0434\u0435\u043d\u043d\u044b\u0439 \u0434\u0435\u0444\u0438\u0446\u0438\u0442 \u043a\u043e\u044d\u043d\u0437\u0438\u043c\u0430 Q10 (\u043f\u0435\u0440\u0432\u0438\u0447\u043d\u044b\u0439). \u0421\u0438\u043c\u043f\u0442\u043e\u043c\u044b \u0432 \u0432\u0438\u0434\u0435 \u043c\u043e\u0437\u0436\u0435\u0447\u043a\u043e\u0432\u043e\u0439 \u0430\u0442\u0430\u043a\u0441\u0438\u0438, \u044d\u043d\u0446\u0435\u0444\u0430\u043b\u043e\u043c\u0438\u043e\u043f\u0430\u0442\u0438\u0438, \u0438\u0437\u043e\u043b\u0438\u0440\u043e\u0432\u0430\u043d\u043d\u043e\u0439 \u043c\u0438\u043e\u043f\u0430\u0442\u0438\u0438. <\/li>\n\n\n\n<li>\u0414\u0440\u0443\u0433\u0438\u0435 \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u044b\u0435 \u0437\u0430\u0431\u043e\u043b\u0435\u0432\u0430\u043d\u0438\u044f (\u0432\u0442\u043e\u0440\u0438\u0447\u043d\u0430\u044f \u043d\u0435\u0434\u043e\u0441\u0442\u0430\u0442\u043e\u0447\u043d\u043e\u0441\u0442\u044c): \n<ul class=\"wp-block-list\">\n<li>\u0410\u0442\u0430\u043a\u0441\u0438\u044f \u0424\u0440\u0438\u0434\u0440\u0438\u0445\u0430.<\/li>\n\n\n\n<li>CPEO (\u0445\u0440\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u043f\u0440\u043e\u0433\u0440\u0435\u0441\u0441\u0438\u0440\u0443\u044e\u0449\u0430\u044f \u0432\u043d\u0435\u0448\u043d\u044f\u044f \u043e\u0444\u0442\u0430\u043b\u044c\u043c\u043e\u043f\u043b\u0435\u0433\u0438\u044f),<\/li>\n\n\n\n<li>\u0414\u0435\u0444\u0438\u0446\u0438\u0442 \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0433\u043e \u043a\u043e\u043c\u043f\u043b\u0435\u043a\u0441\u0430 I. <\/li>\n\n\n\n<li>\u0414\u0435\u0444\u0438\u0446\u0438\u0442 \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0433\u043e \u043a\u043e\u043c\u043f\u043b\u0435\u043a\u0441\u0430 II. <\/li>\n\n\n\n<li>\u0414\u0435\u0444\u0438\u0446\u0438\u0442 \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0433\u043e \u043a\u043e\u043c\u043f\u043b\u0435\u043a\u0441\u0430 II\/IV. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u041a\u0435\u0440\u043d\u0441\u0430-\u0421\u0435\u0439\u0440\u0430. <\/li>\n\n\n\n<li>LHON (\u043d\u0430\u0441\u043b\u0435\u0434\u0441\u0442\u0432\u0435\u043d\u043d\u0430\u044f \u043e\u043f\u0442\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u043d\u0435\u0439\u0440\u043e\u043f\u0430\u0442\u0438\u044f \u041b\u0435\u0431\u0435\u0440\u0430).<\/li>\n\n\n\n<li>MELAS (\u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u0430\u044f \u043c\u0438\u043e\u043f\u0430\u0442\u0438\u044f, \u044d\u043d\u0446\u0435\u0444\u0430\u043b\u043e\u043f\u0430\u0442\u0438\u044f, \u043b\u0430\u043a\u0442\u043e\u0430\u0446\u0438\u0434\u043e\u0437 \u0438 \u0438\u043d\u0441\u0443\u043b\u044c\u0442).<\/li>\n\n\n\n<li>\u041d\u0410\u0420\u041f (\u043d\u0435\u0439\u0440\u043e\u0433\u0435\u043d\u043d\u0430\u044f \u043c\u044b\u0448\u0435\u0447\u043d\u0430\u044f \u0441\u043b\u0430\u0431\u043e\u0441\u0442\u044c, \u0430\u0442\u0430\u043a\u0441\u0438\u044f \u0438 \u043f\u0438\u0433\u043c\u0435\u043d\u0442\u043d\u044b\u0439 \u0440\u0435\u0442\u0438\u043d\u0438\u0442).<\/li>\n\n\n\n<li>\u041c\u0435\u0440\u0446\u0430\u0442\u0435\u043b\u044c\u043d\u044b\u0435 \u0440\u0430\u0441\u0441\u0442\u0440\u043e\u0439\u0441\u0442\u0432\u0430 (C10orf2)<\/li>\n\n\n\n<li>\u0413\u043b\u0430\u0437\u043e\u0434\u0432\u0438\u0433\u0430\u0442\u0435\u043b\u044c\u043d\u0430\u044f \u0430\u043f\u0440\u0430\u043a\u0441\u0438\u044f. <\/li>\n\n\n\n<li>\u041c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u0430\u044f \u043a\u0430\u0440\u0434\u0438\u043e\u043c\u0438\u043e\u043f\u0430\u0442\u0438\u044f. <\/li>\n\n\n\n<li>\u0411\u043e\u043b\u0435\u0437\u043d\u044c \u0410\u043b\u044c\u043f\u0435\u0440\u0441\u0430. <\/li>\n\n\n\n<li>MERRF (\u043c\u0438\u043e\u043a\u043b\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u044d\u043f\u0438\u043b\u0435\u043f\u0441\u0438\u044f, \u0441\u0432\u044f\u0437\u0430\u043d\u043d\u0430\u044f \u0441 \u0440\u0432\u0430\u043d\u044b\u043c\u0438 \u043a\u0440\u0430\u0441\u043d\u044b\u043c\u0438 \u0432\u043e\u043b\u043e\u043a\u043d\u0430\u043c\u0438).<\/li>\n\n\n\n<li>\u0421\u0410\u041d\u0414\u041e (\u0441\u0435\u043d\u0441\u043e\u0440\u043d\u0430\u044f \u0430\u0442\u0430\u043a\u0441\u0438\u044f \u0441 \u043d\u0435\u0439\u0440\u043e\u043f\u0430\u0442\u0438\u0435\u0439, \u0434\u0438\u0437\u0430\u0440\u0442\u0440\u0438\u0435\u0439 \u0438 \u043e\u0444\u0442\u0430\u043b\u044c\u043c\u043e\u043f\u0430\u0440\u0435\u0437\u043e\u043c)<\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0438\u0441\u0442\u043e\u0449\u0435\u043d\u0438\u044f \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0439 \u0414\u041d\u041a. <\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<\/li>\n\n\n\n<li>\u0414\u0440\u0443\u0433\u0438\u0435 \u0437\u0430\u0431\u043e\u043b\u0435\u0432\u0430\u043d\u0438\u044f (\u0432\u0442\u043e\u0440\u0438\u0447\u043d\u0430\u044f \u043d\u0435\u0434\u043e\u0441\u0442\u0430\u0442\u043e\u0447\u043d\u043e\u0441\u0442\u044c): \n<ul class=\"wp-block-list\">\n<li>\u041f\u0440\u043e\u043f\u0438\u043e\u043d\u043e\u0432\u0430\u044f \u0430\u0446\u0438\u0434\u0435\u043c\u0438\u044f. <\/li>\n\n\n\n<li>\u041c\u043d\u043e\u0436\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u0430\u044f \u0441\u0438\u0441\u0442\u0435\u043c\u043d\u0430\u044f \u0430\u0442\u0440\u043e\u0444\u0438\u044f. <\/li>\n\n\n\n<li>\u041a\u043e\u0440\u0442\u0438\u043a\u043e\u0431\u0430\u0437\u0430\u043b\u044c\u043d\u0430\u044f \u0434\u0435\u0433\u0435\u043d\u0435\u0440\u0430\u0446\u0438\u044f. <\/li>\n\n\n\n<li>\u041c\u044b\u0448\u0435\u0447\u043d\u0430\u044f \u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u044f. <\/li>\n\n\n\n<li>\u0411\u043e\u043a\u043e\u0432\u043e\u0439 \u0430\u043c\u0438\u043e\u0442\u0440\u043e\u0444\u0438\u0447\u0435\u0441\u043a\u0438\u0439 \u0441\u043a\u043b\u0435\u0440\u043e\u0437. <\/li>\n\n\n\n<li>\u0420\u0430\u0441\u0441\u0435\u044f\u043d\u043d\u044b\u0439 \u0441\u043a\u043b\u0435\u0440\u043e\u0437. <\/li>\n\n\n\n<li>\u0411\u043e\u043b\u0435\u0437\u043d\u044c \u0428\u0430\u0440\u043a\u043e-\u041c\u0430\u0440\u0438-\u0422\u0443\u0442\u0430.<\/li>\n\n\n\n<li>\u0411\u043e\u043b\u0435\u0437\u043d\u044c \u041c\u0430\u043a\u0410\u0440\u0434\u043b\u0430. <\/li>\n\n\n\n<li>\u041b\u0435\u0439\u043a\u043e\u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u044f. <\/li>\n\n\n\n<li>\u041c\u0438\u0433\u0440\u0435\u043d\u044c. <\/li>\n\n\n\n<li>\u041c\u0438\u043e\u043f\u0430\u0442\u0438\u044f \u0432\u0441\u043b\u0435\u0434\u0441\u0442\u0432\u0438\u0435 \u0434\u0435\u0444\u0438\u0446\u0438\u0442\u0430 \u043c\u0438\u043e\u0430\u0434\u0435\u043d\u0438\u043b\u0430\u0442\u0434\u0435\u0437\u0430\u043c\u0438\u043d\u0430\u0437\u044b (MADA). <\/li>\n\n\n\n<li>\u041f\u0440\u043e\u0433\u0440\u0435\u0441\u0441\u0438\u0440\u0443\u044e\u0449\u0438\u0439 \u043d\u0430\u0434\u044a\u044f\u0434\u0435\u0440\u043d\u044b\u0439 \u043f\u0430\u0440\u0430\u043b\u0438\u0447. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0446\u0438\u043a\u043b\u0438\u0447\u0435\u0441\u043a\u043e\u0439 \u0440\u0432\u043e\u0442\u044b. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0421\u0430\u043d\u0444\u0438\u043b\u0438\u043f\u043f\u043e. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0412\u043e\u043b\u044c\u0444\u0430-\u0425\u0438\u0440\u0448\u0445\u043e\u0440\u043d\u0430. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0411\u0430\u0440\u0434\u0435-\u0411\u0438\u0434\u043b\u044f. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0445\u0440\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u043e\u0439 \u0443\u0441\u0442\u0430\u043b\u043e\u0441\u0442\u0438. <\/li>\n\n\n\n<li>\u0413\u043b\u0430\u0434\u0438\u0442\u044c. <\/li>\n\n\n\n<li>\u0410\u0434\u0440\u0435\u043d\u043e\u043b\u0435\u0439\u043a\u043e\u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u044f. <\/li>\n\n\n\n<li>\u0421\u043f\u0438\u043d\u043e\u0446\u0435\u0440\u0435\u0431\u0435\u043b\u043b\u044f\u0440\u043d\u0430\u044f \u0430\u0442\u0430\u043a\u0441\u0438\u044f. <\/li>\n\n\n\n<li>\u0414\u0435\u0444\u0438\u0446\u0438\u0442 \u0444\u043e\u043b\u0438\u0435\u0432\u043e\u0439 \u043a\u0438\u0441\u043b\u043e\u0442\u044b.<\/li>\n\n\n\n<li>\u041e\u043a\u0443\u043b\u043e\u0444\u0430\u0440\u0438\u043d\u0433\u0435\u0430\u043b\u044c\u043d\u0430\u044f \u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u044f. <\/li>\n\n\n\n<li>\u041c\u0438\u043e\u0442\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u044f \u0428\u0442\u0435\u0439\u043d\u0435\u0440\u0442\u0430. <\/li>\n\n\n\n<li>\u0411\u043e\u043b\u0435\u0437\u043d\u044c \u0425\u0430\u043d\u0442\u0438\u043d\u0433\u0442\u043e\u043d\u0430. <\/li>\n\n\n\n<li>\u0411\u043e\u043b\u0435\u0437\u043d\u044c \u041d\u0438\u043c\u0430\u043d\u0430-\u041f\u0438\u043a\u0430.<\/li>\n\n\n\n<li>\u0411\u043e\u043b\u0435\u0437\u043d\u044c \u041f\u043e\u043c\u043f\u0435. <\/li>\n\n\n\n<li>\u0421\u043f\u0430\u0441\u0442\u0438\u0447\u043d\u043e\u0441\u0442\u044c. <\/li>\n\n\n\n<li>\u0421\u043f\u0430\u0441\u0442\u0438\u0447\u0435\u0441\u043a\u0438\u0439 \u043f\u0430\u0440\u0430\u043f\u0430\u0440\u0435\u0437. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u041f\u0440\u0430\u0434\u0435\u0440\u0430-\u0412\u0438\u043b\u043b\u0438. <\/li>\n\n\n\n<li>\u0421\u0438\u043d\u0434\u0440\u043e\u043c \u0412\u043e\u043b\u044c\u0444\u0440\u0430\u043c\u0430. <\/li>\n<\/ul>\n<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>https:\/\/www.frontiersin.org\/articles\/10.3389\/fnins.2023.1188839\/full https:\/\/metabolicas.sjdhospitalbarcelona.org\/ecm\/defectos-sintesis-coenzima-q10\/info\/como-diagnostica-deficiencia-coenzima-q10 https:\/\/www.aeped.es\/comite-medicamentos\/pediamecum\/coenzima-q10-ubidecarenona Indicaciones de tratamiento en neurolog\u00eda pedi\u00e1trica:<\/p>","protected":false},"author":1,"featured_media":6314,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[24,7,17],"tags":[],"class_list":["post-6313","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-farmacos","category-metabolismo","category-tratamiento","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/posts\/6313","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/comments?post=6313"}],"version-history":[{"count":2,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/posts\/6313\/revisions"}],"predecessor-version":[{"id":6316,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/posts\/6313\/revisions\/6316"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/media\/6314"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/media?parent=6313"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/categories?post=6313"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/ru\/wp-json\/wp\/v2\/tags?post=6313"}],"curies":[{"name":"WP","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}