{"id":4523,"date":"2023-02-19T18:10:27","date_gmt":"2023-02-19T18:10:27","guid":{"rendered":"https:\/\/neuropediatoolbox.org\/?p=4523"},"modified":"2026-06-22T16:28:58","modified_gmt":"2026-06-22T16:28:58","slug":"trayectoria-de-desarrollo-de-la-mld-leucodistrofia-metacromatica","status":"publish","type":"post","link":"https:\/\/neuropediatoolkit.org\/zh\/trayectoria-de-desarrollo-de-la-mld-leucodistrofia-metacromatica\/","title":{"rendered":"MLD\uff08\u5f02\u67d3\u6027\u8111\u767d\u8d28\u8425\u517b\u4e0d\u826f\uff09\u7684\u53d1\u5c55\u8f68\u8ff9\u3002"},"content":{"rendered":"<h2 class=\"wp-block-heading\">\u5f02\u67d3\u6027\u8111\u767d\u8d28\u8425\u517b\u4e0d\u826f (MLD)\uff1a\u53d1\u80b2\u8f68\u8ff9<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">\u5f02\u67d3\u6027\u8111\u767d\u8d28\u8425\u517b\u4e0d\u826f\u662f\u4e00\u79cd\u5e38\u67d3\u8272\u4f53\u9690\u6027\u9057\u4f20\u6027\u6eb6\u9176\u4f53\u8d2e\u79ef\u75c5\uff0c\u5176\u7279\u5f81\u662f\u82b3\u57fa\u786b\u9178\u916f\u9176 A (ARSA) \u7f3a\u4e4f\uff0c\u5bfc\u81f4\u8111\u786b\u82f7\u8102\u79ef\u805a\u4ee5\u53ca\u4e2d\u67a2\u548c\u5468\u56f4\u795e\u7ecf\u7cfb\u7edf\u8fdb\u884c\u6027\u8131\u9ad3\u9798\u3002<\/p>\n\n\n\n<h3 class=\"wp-block-heading\">\u4e34\u5e8a\u5f62\u5f0f\u548c\u8f68\u8ff9<\/h3>\n\n\n\n<ul class=\"wp-block-list\">\n    <li><strong>\u665a\u671f\u5a74\u513f\uff08\u5178\u578b\uff09\uff1a<\/strong> \u5b83\u51fa\u73b0\u5728\u751f\u547d\u7684\u7b2c\u4e00\u5e74\u548c\u7b2c\u4e8c\u5e74\u4e4b\u95f4\u3002\u5a74\u513f\u4e27\u5931\u540e\u5929\u884c\u8d70\u80fd\u529b\uff0c\u51fa\u73b0\u4e25\u91cd\u7684\u8fd0\u52a8\u9000\u5316\u3001\u8fdb\u884c\u6027\u75c9\u631b\u6027\u56db\u80a2\u762b\u75ea\u548c\u5931\u660e\u3002<\/li>\n    <li><strong>\u9752\u5c11\u5e74\u548c\u6210\u4eba\uff1a<\/strong> \u8fdb\u5c55\u7f13\u6162\uff0c\u6700\u521d\u7684\u7279\u70b9\u662f\u5b66\u4e60\u56f0\u96be\u3001\u884c\u4e3a\u969c\u788d\u3001\u5171\u6d4e\u5931\u8c03\u548c\u968f\u540e\u7684\u6574\u4f53\u8fd0\u52a8\u969c\u788d\u3002<\/li>\n<\/ul>","protected":false},"excerpt":{"rendered":"<p>\u5f02\u67d3\u6027\u8111\u767d\u8d28\u8425\u517b\u4e0d\u826f (MLD)\uff1a\u53d1\u80b2\u8f68\u8ff9 \u5f02\u67d3\u6027\u8111\u767d\u8d28\u8425\u517b\u4e0d\u826f\u662f\u4e00\u79cd\u5e38\u67d3\u8272\u4f53\u9690\u6027\u9057\u4f20\u6027\u6eb6\u9176\u4f53\u8d2e\u79ef\u75c5\uff0c\u5176\u7279\u5f81\u662f\u82b3\u57fa\u786b\u9178\u916f\u9176 A (ARSA) \u7f3a\u4e4f\uff0c\u5bfc\u81f4\u8111\u786b\u82f7\u8102\u79ef\u805a\u4ee5\u53ca\u4e2d\u67a2\u548c\u5468\u56f4\u795e\u7ecf\u7cfb\u7edf\u8fdb\u884c\u6027\u8131\u9ad3\u9798\u3002\u4e34\u5e8a\u5f62\u5f0f\u548c\u7ae5\u5e74\u665a\u671f\u8f68\u8ff9\uff08\u5178\u578b\uff09\uff1a\u5b83\u8868\u73b0\u5728\u7b2c\u4e00\u6b21\u2026\u2026\u4e4b\u95f4 <\/p>\n<p class=\"link-more\"><a href=\"https:\/\/neuropediatoolkit.org\/zh\/trayectoria-de-desarrollo-de-la-mld-leucodistrofia-metacromatica\/\" class=\"more-link\">\u7ee7\u7eed\u9605\u8bfb<span class=\"screen-reader-text\"> \u201cMLD\uff08\u5f02\u67d3\u6027\u8111\u767d\u8d28\u8425\u517b\u4e0d\u826f\uff09\u7684\u53d1\u5c55\u8f68\u8ff9\u3002\u201d<\/span><\/a><\/p>","protected":false},"author":1,"featured_media":4525,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_themeisle_gutenberg_block_has_review":false,"footnotes":""},"categories":[49],"tags":[],"class_list":["post-4523","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-neurodegenerativas","entry"],"_links":{"self":[{"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/posts\/4523","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/comments?post=4523"}],"version-history":[{"count":2,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/posts\/4523\/revisions"}],"predecessor-version":[{"id":8292,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/posts\/4523\/revisions\/8292"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/media\/4525"}],"wp:attachment":[{"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/media?parent=4523"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/categories?post=4523"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/neuropediatoolkit.org\/zh\/wp-json\/wp\/v2\/tags?post=4523"}],"curies":[{"name":"\u53ef\u6e7f\u6027\u7c89\u5242","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}